In:
Jornal de Pneumologia, FapUNIFESP (SciELO), Vol. 29, No. 5 ( 2003-10), p. 302-304
Abstract:
Severe pulmonary hypertension is a debilitating disease with short life expectancy that often affects young people. Pleuropulmonary complications of systemic lupus erythematosus occur in 50-70% of patients. Severe symptomatic pulmonary hypertension in systemic lupus erythematosus is rare and carries a bad prognosis because a fatal outcome can occur within months. The authors describe, for the first time, a patient with systemic lupus erythematosus with severe pulmonary hypertension and secondary antiphospholipid syndrome who responded favorably to oral sildenafil, after unsuccessful use of prednisone, intravenous cyclophosphamide, warfarin and diltiazem.
Type of Medium:
Online Resource
ISSN:
0102-3586
DOI:
10.1590/S0102-35862003000500009
Language:
Unknown
Publisher:
FapUNIFESP (SciELO)
Publication Date:
2003
detail.hit.zdb_id:
2105641-9
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