In:
Texas Heart Institute Journal, Texas Heart Institute Journal, Vol. 44, No. 1 ( 2017-02-01), p. 50-54
Abstract:
Renal artery stenosis caused by neurofibromatosis is a rare cause of renovascular hypertension. This hypertension can develop during childhood and is one of the leading causes of poor outcome. We report the case of a 17-year-old girl who was incidentally diagnosed with severe hypertension. During her examination for secondary hypertension, we reached a diagnosis of neurofibromatosis type 1 on the basis of a cluster of typical findings: optic nerve glioma, café au lait spots, nodular neurofibromas, and axillary freckling. Renal angiograms revealed a hemodynamically significant left renal artery stenosis (70%). Renal angioplasty with a self-expanding stent was performed one month later for rapidly progressive renal artery stenosis (90%) and uncontrolled blood pressure. Excellent blood pressure control resulted immediately and was maintained as of the 2-year follow-up evaluation. We think that percutaneous transluminal renal angioplasty can be effective in select patients who have neurofibromatosis type 1 and refractory hypertension caused by renal artery stenosis.
Type of Medium:
Online Resource
ISSN:
0730-2347
,
1526-6702
DOI:
10.14503/THIJ-15-5466
Language:
English
Publisher:
Texas Heart Institute Journal
Publication Date:
2017
detail.hit.zdb_id:
2068440-X
Permalink
